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Nucleolar expansion and elevated protein translation in premature aging

Premature aging disorders provide an opportunity to study the mechanisms that drive aging. In Hutchinson-Gilford progeria syndrome (HGPS), a mutant form of the nuclear scaffold protein lamin A distorts nuclei and sequesters nuclear proteins. We sought to investigate protein homeostasis in this disea...

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Publicat a:Nat Commun
Autors principals: Buchwalter, Abigail, Hetzer, Martin W.
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group UK 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5577202/
https://ncbi.nlm.nih.gov/pubmed/28855503
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41467-017-00322-z
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