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Drosophila models of prionopathies: insight into prion protein function, transmission, and neurotoxicity

Prion diseases (PrD) are unique neurodegenerative conditions that can present with sporadic, genetic, and infectious etiologies. The agent responsible for these pathologies in humans and mammals is a misfolded conformation of the prion protein (PrP), a membrane-anchored protein highly expressed in t...

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Dades bibliogràfiques
Publicat a:Curr Opin Genet Dev
Autors principals: Fernandez-Funez, Pedro, Sanchez-Garcia, Jonatan, Rincon-Limas, Diego E.
Format: Artigo
Idioma:Inglês
Publicat: 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5474952/
https://ncbi.nlm.nih.gov/pubmed/28415023
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.gde.2017.03.013
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