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MEK inhibition appears to improve symptom control in primary NRAS-driven CNS melanoma in children

BACKGROUND: Primary melanoma of the CNS in children is extremely rare, and usually linked to congenital melanocytic naevus syndrome, caused by mosaicism for oncogenic NRAS mutations. Outcome is fatal in all cases. Data from murine and in vitro studies suggest that MEK inhibition is a possible therap...

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Dettagli Bibliografici
Pubblicato in:Br J Cancer
Autori principali: Kinsler, Veronica A, O'Hare, Patricia, Jacques, Thomas, Hargrave, Darren, Slater, Olga
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5396107/
https://ncbi.nlm.nih.gov/pubmed/28253523
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/bjc.2017.49
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