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C1q ablation exacerbates amyloid deposition: A study in a transgenic mouse model of ATTRV30M amyloid neuropathy

ATTRV30M amyloid neuropathy is a lethal autosomal dominant sensorimotor and autonomic neuropathy, caused by deposition of amyloid fibrils composed of aberrant transthyretin (TTR). Ages of onset and penetrance exhibit great variability and genetic factors have been implicated. Complement activation c...

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Dettagli Bibliografici
Pubblicato in:PLoS One
Autori principali: Panayiotou, Elena, Fella, Eleni, Papacharalambous, Revekka, Malas, Stavros, Saraiva, Maria Joao, Kyriakides, Theodoros
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5391113/
https://ncbi.nlm.nih.gov/pubmed/28407005
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0175767
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