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Quick Diagnosis of Alkaptonuria by Homogentisic Acid Determination in Urine Paper Spots

Objectives: Two methods are described for homogentisic acid (HGA) determination in dried urine spots (DUS) on paper from Alkaptonuria (AKU) patients, devised for quick early diagnosis. AKU is a rare autosomal recessive disorder caused by deficiency of homogentisate 1,2-dioxygenase, yielding in accum...

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書目詳細資料
發表在:JIMD Rep
Main Authors: Jacomelli, Gabriella, Micheli, Vanna, Bernardini, Giulia, Millucci, Lia, Santucci, Annalisa
格式: Artigo
語言:Inglês
出版: Springer Berlin Heidelberg 2016
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在線閱讀:https://ncbi.nlm.nih.gov/pmc/articles/PMC5388646/
https://ncbi.nlm.nih.gov/pubmed/27074788
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2016_554
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