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Decreased Levels of Foldase and Chaperone Proteins Are Associated with an Early-Onset Amyotrophic Lateral Sclerosis

Amyotrophic lateral sclerosis (ALS) is a fatal neurodegenerative disease characterized by a progressive upper and lower motor neuron degeneration. One of the peculiar clinical characteristics of ALS is the wide distribution in age of onset, which is probably caused by different combinations of intri...

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Detalhes bibliográficos
Publicado no:Front Mol Neurosci
Main Authors: Filareti, Melania, Luotti, Silvia, Pasetto, Laura, Pignataro, Mauro, Paolella, Katia, Messina, Paolo, Pupillo, Elisabetta, Filosto, Massimiliano, Lunetta, Christian, Mandrioli, Jessica, Fuda, Giuseppe, Calvo, Andrea, Chiò, Adriano, Corbo, Massimo, Bendotti, Caterina, Beghi, Ettore, Bonetto, Valentina
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5382314/
https://ncbi.nlm.nih.gov/pubmed/28428745
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2017.00099
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