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Amyotrophic lateral sclerosis-linked mutations increase the viscosity of liquid-like TDP-43 RNP granules in neurons

Ribonucleoprotein (RNP) granules are enriched in specific RNAs and RNA-binding proteins (RBPs) and mediate critical cellular processes. Purified RBPs form liquid droplets in vitro through liquid–liquid phase separation and liquid-like non–membrane-bound structures in cells. Mutations in the human RB...

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Bibliografske podrobnosti
izdano v:Proc Natl Acad Sci U S A
Main Authors: Gopal, Pallavi P., Nirschl, Jeffrey J., Klinman, Eva, Holzbaur, Erika L. F.
Format: Artigo
Jezik:Inglês
Izdano: National Academy of Sciences 2017
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC5373408/
https://ncbi.nlm.nih.gov/pubmed/28265061
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1614462114
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