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Post-translational modifications in PrP expand the conformational diversity of prions in vivo

Misfolded prion protein aggregates (PrP(Sc)) show remarkable structural diversity and are associated with highly variable disease phenotypes. Similarly, other proteins, including amyloid-β, tau, α-synuclein, and serum amyloid A, misfold into distinct conformers linked to different clinical diseases...

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Detalles Bibliográficos
Publicado en:Sci Rep
Main Authors: Aguilar-Calvo, Patricia, Xiao, Xiangzhu, Bett, Cyrus, Eraña, Hasier, Soldau, Katrin, Castilla, Joaquin, Nilsson, K. Peter R., Surewicz, Witold K., Sigurdson, Christina J.
Formato: Artigo
Idioma:Inglês
Publicado: Nature Publishing Group 2017
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5341109/
https://ncbi.nlm.nih.gov/pubmed/28272426
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep43295
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