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Post-translational modifications in PrP expand the conformational diversity of prions in vivo

Misfolded prion protein aggregates (PrP(Sc)) show remarkable structural diversity and are associated with highly variable disease phenotypes. Similarly, other proteins, including amyloid-β, tau, α-synuclein, and serum amyloid A, misfold into distinct conformers linked to different clinical diseases...

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Dettagli Bibliografici
Pubblicato in:Sci Rep
Autori principali: Aguilar-Calvo, Patricia, Xiao, Xiangzhu, Bett, Cyrus, Eraña, Hasier, Soldau, Katrin, Castilla, Joaquin, Nilsson, K. Peter R., Surewicz, Witold K., Sigurdson, Christina J.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5341109/
https://ncbi.nlm.nih.gov/pubmed/28272426
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep43295
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