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Increased Ubqln2 Expression Causes Neuron Death in Transgenic Rats

Pathogenic mutation of ubiquilin 2 (UBQLN2) causes neurodegeneration in amyotrophic lateral sclerosis and frontotemporal lobar degeneration. How UBQLN2 mutations cause the diseases is not clear. While overexpression of UBQLN2 with pathogenic mutation causes neuron death in rodent models, deletion of...

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Dades bibliogràfiques
Publicat a:J Neurochem
Autors principals: Huang, Bo, Wu, Qinxue, Zhou, Hongxia, Huang, Cao, Xia, Xu-Gang
Format: Artigo
Idioma:Inglês
Publicat: 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5117623/
https://ncbi.nlm.nih.gov/pubmed/27456931
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/jnc.13748
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