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Mitochondrial damage revealed by immunoselection for ALS-linked misfolded SOD1

Mutant superoxide dismutase 1 (SOD1) selectively associates with spinal cord mitochondria in rodent models of SOD1-mediated amyotrophic lateral sclerosis. A portion of mutant SOD1 exists in a non-native/misfolded conformation that is selectively recognized by conformational antibodies. Misfolded SOD...

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Dettagli Bibliografici
Pubblicato in:Hum Mol Genet
Autori principali: Pickles, Sarah, Destroismaisons, Laurie, Peyrard, Sarah L., Cadot, Sarah, Rouleau, Guy A., Brown, Robert H., Julien, Jean-Pierre, Arbour, Nathalie, Velde, Christine Vande
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5052069/
https://ncbi.nlm.nih.gov/pubmed/23736301
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddt249
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