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Evidence for defective energy homeostasis in amyotrophic lateral sclerosis: Benefit of a high-energy diet in a transgenic mouse model

Amyotrophic lateral sclerosis (ALS) is an adult-onset neurodegenerative disease characterized by selective loss of motor neurons and progressive muscle wasting. Growing evidence indicates that mitochondrial dysfunction, not only occurring in motor neurons but also in skeletal muscle, may play a cruc...

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Detalhes bibliográficos
Main Authors: Dupuis, Luc, Oudart, Hugues, René, Frédérique, de Aguilar, Jose-Luis Gonzalez, Loeffler, Jean-Philippe
Formato: Artigo
Idioma:Inglês
Publicado em: National Academy of Sciences 2004
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC503756/
https://ncbi.nlm.nih.gov/pubmed/15263088
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0402026101
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