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DNA Damage Response and DNA Repair in Skeletal Myocytes From a Mouse Model of Spinal Muscular Atrophy

We studied DNA damage response (DDR) and DNA repair capacities of skeletal muscle cells from a mouse model of infantile spinal muscular atrophy (SMA) caused by loss-of-function mutation of survival of motor neuron (Smn). Primary myocyte cultures derived from skeletal muscle satellite cells of neonat...

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Detalles Bibliográficos
Publicado en:J Neuropathol Exp Neurol
Main Authors: Fayzullina, Saniya, Martin, Lee J.
Formato: Artigo
Idioma:Inglês
Publicado: Oxford University Press 2016
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5015659/
https://ncbi.nlm.nih.gov/pubmed/27452406
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/jnen/nlw064
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