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Neutrophil elastase and matrix metalloproteinase 12 in cystic fibrosis lung disease

Chronic lung disease remains the major cause of morbidity and mortality in patients with cystic fibrosis (CF). Recent studies in young children with CF diagnosed by newborn screening identified neutrophil elastase (NE), a major product released from neutrophils in inflamed airways, as a key risk fac...

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Pubblicato in:Mol Cell Pediatr
Autori principali: Wagner, Claudius J., Schultz, Carsten, Mall, Marcus A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer Berlin Heidelberg 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4960106/
https://ncbi.nlm.nih.gov/pubmed/27456476
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s40348-016-0053-7
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