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Tighter Control by Chymotrypsin C (CTRC) Explains Lack of Association between Human Anionic Trypsinogen and Hereditary Pancreatitis

The human pancreas expresses two major trypsinogen isoforms, cationic trypsinogen (PRSS1) and anionic trypsinogen (PRSS2). Mutations in PRSS1 cause hereditary pancreatitis by altering cleavage of regulatory nick sites by chymotrypsin C (CTRC) resulting in reduced trypsinogen degradation and increase...

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Publicado en:J Biol Chem
Autores principales: Jancsó, Zsanett, Sahin-Tóth, Miklós
Formato: Artigo
Lenguaje:Inglês
Publicado: American Society for Biochemistry and Molecular Biology 2016
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4933207/
https://ncbi.nlm.nih.gov/pubmed/27129265
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M116.725374
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