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Revisiting the Heidenhain Variant of Creutzfeldt-Jakob Disease: Evidence for Prion Type Variability Influencing Clinical Course and Laboratory Findings

The Heidenhain variant defines a peculiar clinical presentation of sporadic Creutzfeldt-Jakob disease (sCJD) characterized by isolated visual disturbances at disease onset and reflecting the early targeting of prions to the occipital cortex. Molecular and histopathological typing, thus far performed...

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Détails bibliographiques
Publié dans:J Alzheimers Dis
Auteurs principaux: Baiardi, Simone, Capellari, Sabina, Ladogana, Anna, Strumia, Silvia, Santangelo, Mario, Pocchiari, Maurizio, Parchi, Piero
Format: Artigo
Langue:Inglês
Publié: IOS Press 2015
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4927903/
https://ncbi.nlm.nih.gov/pubmed/26682685
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/JAD-150668
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