Caricamento...

Characterization of Truncated Forms of Abnormal Prion Protein in Creutzfeldt-Jakob Disease

In prion disease, the abnormal conformer of the cellular prion protein, PrP(Sc), deposits in fibrillar protein aggregates in brain and other organs. Limited exposure of PrP(Sc) to proteolytic digestion in vitro generates a core fragment of 19–21 kDa, named PrP27–30, which is also found in vivo. Rece...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Autori principali: Notari, Silvio, Strammiello, Rosaria, Capellari, Sabina, Giese, Armin, Cescatti, Maura, Grassi, Jacques, Ghetti, Bernardino, Langeveld, Jan P. M., Zou, Wen-Quan, Gambetti, Pierluigi, Kretzschmar, Hans A., Parchi, Piero
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Biochemistry and Molecular Biology 2008
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2662149/
https://ncbi.nlm.nih.gov/pubmed/18753138
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M801877200
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !