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Direct Molecular Diagnosis of CYP21A2 Point Mutations in Macedonian and Serbian Patients with 21-Hydroxylase Deficiency

BACKGROUND: Steroid 21-hydroxylase deficiency is present in 90–95% of all cases with congenital adrenal hyperplasia (CAH), an autosomal recessive disorder. It can present as the severe classical salt wasting (SW) or simple virilising (SV) form, or the milder, nonclassical form. Nine pseudogene-deriv...

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Bibliografski detalji
Izdano u:J Med Biochem
Glavni autori: Anastasovska, Violeta, Milenković, Tatjana, Kocova, Mirjana
Format: Artigo
Jezik:Inglês
Izdano: Society of Medical Biochemists of Serbia 2015
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4922339/
https://ncbi.nlm.nih.gov/pubmed/28356824
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2478/jomb-2014-0048
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