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Direct Molecular Diagnosis of CYP21A2 Point Mutations in Macedonian and Serbian Patients with 21-Hydroxylase Deficiency

BACKGROUND: Steroid 21-hydroxylase deficiency is present in 90–95% of all cases with congenital adrenal hyperplasia (CAH), an autosomal recessive disorder. It can present as the severe classical salt wasting (SW) or simple virilising (SV) form, or the milder, nonclassical form. Nine pseudogene-deriv...

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Dades bibliogràfiques
Publicat a:J Med Biochem
Autors principals: Anastasovska, Violeta, Milenković, Tatjana, Kocova, Mirjana
Format: Artigo
Idioma:Inglês
Publicat: Society of Medical Biochemists of Serbia 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4922339/
https://ncbi.nlm.nih.gov/pubmed/28356824
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2478/jomb-2014-0048
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