On the mechanism of gating defects caused by the R117H mutation in cystic fibrosis transmembrane conductance regulator

Ítems similars

• Structural mechanisms for defective CFTR gating caused by the Q1412X mutation, a severe Class VI pathogenic mutation in cystic fibrosis
  per: Yeh, Jiunn‐Tyng, et al.
  Publicat: (2018)
• Synergistic Potentiation of Cystic Fibrosis Transmembrane Conductance Regulator Gating by Two Chemically Distinct Potentiators, Ivacaftor (VX-770) and 5-Nitro-2-(3-Phenylpropylamino) Benzoate
  per: Lin, Wen-Ying, et al.
  Publicat: (2016)
• Dual Activity of Aminoarylthiazoles on the Trafficking and Gating Defects of the Cystic Fibrosis Transmembrane Conductance Regulator Chloride Channel Caused by Cystic Fibrosis Mutations
  per: Pedemonte, Nicoletta, et al.
  Publicat: (2011)
• Direct effects of 9-anthracene compounds on cystic fibrosis transmembrane conductance regulator gating
  per: Ai, T., et al.
  Publicat: (2004)
• Three-dimensional Reconstruction of Human Cystic Fibrosis Transmembrane Conductance Regulator Chloride Channel Revealed an Ellipsoidal Structure with Orifices beneath the Putative Transmembrane Domain
  per: Mio, Kazuhiro, et al.
  Publicat: (2008)