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The HSP70 co-chaperone DNAJC14 targets misfolded pendrin for unconventional protein secretion

Mutations in SLC26A4, which encodes pendrin, are responsible for hearing loss with an enlarged vestibular aqueduct and Pendred syndrome. The most prevalent mutation in East Asia is p.H723R (His723Arg), which leads to defects in protein folding and cell-surface expression. Here we show that H723R-pen...

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Pubblicato in:Nat Commun
Autori principali: Jung, Jinsei, Kim, Jiyoon, Roh, Shin Hye, Jun, Ikhyun, Sampson, Robert D., Gee, Heon Yung, Choi, Jae Young, Lee, Min Goo
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4848490/
https://ncbi.nlm.nih.gov/pubmed/27109633
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/ncomms11386
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