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Disulfide Mispairing During Proinsulin Folding in the Endoplasmic Reticulum

Proinsulin folding within the endoplasmic reticulum (ER) remains incompletely understood, but it is clear that in mutant INS gene–induced diabetes of youth (MIDY), progression of the (three) native disulfide bonds of proinsulin becomes derailed, causing insulin deficiency, β-cell ER stress, and onse...

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Dettagli Bibliografici
Pubblicato in:Diabetes
Autori principali: Haataja, Leena, Manickam, Nandini, Soliman, Ann, Tsai, Billy, Liu, Ming, Arvan, Peter
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Diabetes Association 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4806660/
https://ncbi.nlm.nih.gov/pubmed/26822090
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2337/db15-1345
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