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Impaired striatal function in Huntington's disease is due to aberrant p75NTR signaling

Huntington's disease (HD) is a rare genetic neurodegenerative disorder for which there is currently no cure. Early hyperkinetic motor symptoms are consistent with reduced activity of indirect pathway striatal projection neurons (iSPNs) responsible for suppression of unwanted actions. Our recent...

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Dades bibliogràfiques
Publicat a:Rare Dis
Autors principals: Plotkin, Joshua L, Surmeier, D James
Format: Artigo
Idioma:Inglês
Publicat: Taylor & Francis 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4755240/
https://ncbi.nlm.nih.gov/pubmed/26942104
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4161/2167549X.2014.968482
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