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Untreated Congenital Adrenal Hyperplasia with 17-α Hydroxylase/17,20-Lyase Deficiency Presenting as Massive Adrenocortical Tumor

Congenital adrenal hyperplasia (CAH) with 17α-hydroxylase/17,20-lyase deficiency is usually characterized by hypertension and primary amenorrhea, sexual infantilism in women, and pseudohermaphroditism in men. hypertension, and sexual infantilism in women and pseudohermaphroditism in men. In rare cas...

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Bibliographische Detailangaben
Veröffentlicht in:Endocrinol Metab (Seoul)
Hauptverfasser: Lee, Su Jin, Song, Je Eun, Hwang, Sena, Lee, Ji-Yeon, Park, Hye-Sun, Han, Seunghee, Rhee, Yumie
Format: Artigo
Sprache:Inglês
Veröffentlicht: Korean Endocrine Society 2015
Schlagworte:
Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC4595368/
https://ncbi.nlm.nih.gov/pubmed/26248854
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3803/EnM.2015.30.3.408
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