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Untreated Congenital Adrenal Hyperplasia with 17-α Hydroxylase/17,20-Lyase Deficiency Presenting as Massive Adrenocortical Tumor

Congenital adrenal hyperplasia (CAH) with 17α-hydroxylase/17,20-lyase deficiency is usually characterized by hypertension and primary amenorrhea, sexual infantilism in women, and pseudohermaphroditism in men. hypertension, and sexual infantilism in women and pseudohermaphroditism in men. In rare cas...

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Dettagli Bibliografici
Pubblicato in:Endocrinol Metab (Seoul)
Autori principali: Lee, Su Jin, Song, Je Eun, Hwang, Sena, Lee, Ji-Yeon, Park, Hye-Sun, Han, Seunghee, Rhee, Yumie
Natura: Artigo
Lingua:Inglês
Pubblicazione: Korean Endocrine Society 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4595368/
https://ncbi.nlm.nih.gov/pubmed/26248854
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3803/EnM.2015.30.3.408
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