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Untreated Congenital Adrenal Hyperplasia with 17-α Hydroxylase/17,20-Lyase Deficiency Presenting as Massive Adrenocortical Tumor

Congenital adrenal hyperplasia (CAH) with 17α-hydroxylase/17,20-lyase deficiency is usually characterized by hypertension and primary amenorrhea, sexual infantilism in women, and pseudohermaphroditism in men. hypertension, and sexual infantilism in women and pseudohermaphroditism in men. In rare cas...

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Détails bibliographiques
Publié dans:Endocrinol Metab (Seoul)
Auteurs principaux: Lee, Su Jin, Song, Je Eun, Hwang, Sena, Lee, Ji-Yeon, Park, Hye-Sun, Han, Seunghee, Rhee, Yumie
Format: Artigo
Langue:Inglês
Publié: Korean Endocrine Society 2015
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4595368/
https://ncbi.nlm.nih.gov/pubmed/26248854
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3803/EnM.2015.30.3.408
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