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MITOCHONDRIAL DISEASES PART III: THERAPEUTIC INTERVENTIONS IN MOUSE MODELS OF OXPHOS DEFICIENCIES

Mitochondrial defects are the cause of numerous disorders affecting the oxidative phosphorylation system (OXPHOS) in humans leading predominantly to neurological and muscular degeneration. The molecular origin, manifestations, and progression of mitochondrial diseases have a broad spectrum, which ma...

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Publicat a:Mitochondrion
Autors principals: Peralta, Susana, Torraco, Alessandra, Iommarini, Luisa, Diaz, Francisca
Format: Artigo
Idioma:Inglês
Publicat: 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4516588/
https://ncbi.nlm.nih.gov/pubmed/25638392
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.mito.2015.01.007
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