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MITOCHONDRIAL DISEASES PART III: THERAPEUTIC INTERVENTIONS IN MOUSE MODELS OF OXPHOS DEFICIENCIES

Mitochondrial defects are the cause of numerous disorders affecting the oxidative phosphorylation system (OXPHOS) in humans leading predominantly to neurological and muscular degeneration. The molecular origin, manifestations, and progression of mitochondrial diseases have a broad spectrum, which ma...

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Pubblicato in:Mitochondrion
Autori principali: Peralta, Susana, Torraco, Alessandra, Iommarini, Luisa, Diaz, Francisca
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4516588/
https://ncbi.nlm.nih.gov/pubmed/25638392
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.mito.2015.01.007
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