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Nutritional Interventions for Mitochondrial OXPHOS Deficiencies: Mechanisms and Model Systems

Multi-system metabolic disorders caused by defects in oxidative phosphorylation (OXPHOS) are progressive and severely crippling, often lethal, conditions. Inborn errors of OXPHOS function are termed Primary Mitochondrial Disorders (PMDs), and the use of nutritional interventions is routine in PMD su...

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Detaylı Bibliyografya
Yayımlandı:Annu Rev Pathol
Asıl Yazarlar: Kuszak, Adam J., Espey, Michael Graham, Falk, Marni J., Holmbeck, Marissa A., Manfredi, Giovanni, Shadel, Gerald S., Vernon, Hilary J., Zolkipli-Cunningham, Zarazuela
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 2017
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC5911915/
https://ncbi.nlm.nih.gov/pubmed/29099651
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1146/annurev-pathol-020117-043644
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