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Ubiquitin-specific protease 14 modulates degradation of cellular prion protein

Prion diseases are fatal neurodegenerative disorders characterized by the accumulation of prion protein (PrP(C)). To date, there is no effective treatment for the disease. The accumulated PrP, termed PrP(Sc), forms amyloid fibrils and could be infectious. It has been suggested that PrP(Sc) is abnorm...

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Dettagli Bibliografici
Pubblicato in:Sci Rep
Autori principali: Homma, Takujiro, Ishibashi, Daisuke, Nakagaki, Takehiro, Fuse, Takayuki, Mori, Tsuyoshi, Satoh, Katsuya, Atarashi, Ryuichiro, Nishida, Noriyuki
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4462021/
https://ncbi.nlm.nih.gov/pubmed/26061634
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep11028
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