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Mild Lesch–Nyhan Disease in a Boy with a Null Mutation in HPRT1: An Exception to the Known Genotype–Phenotype Correlation

Hypoxanthine–guanine phosphoribosyltransferase (HPRT) deficiency results in a continuous spectrum of clinical phenotypes though all include overproduction of uric acid with hyperuricaemia, urate nephrolithiasis and gout. HPRT1 mutations that result in very low or no HPRT enzyme activities are genera...

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Bibliografski detalji
Izdano u:JIMD Rep
Glavni autori: Bayat, Allan, Christensen, Mette, Wibrand, Flemming, Duno, Morten, Lund, Allan
Format: Artigo
Jezik:Inglês
Izdano: Springer Berlin Heidelberg 2014
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4361920/
https://ncbi.nlm.nih.gov/pubmed/25366392
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2014_368
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