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Mild Lesch–Nyhan Disease in a Boy with a Null Mutation in HPRT1: An Exception to the Known Genotype–Phenotype Correlation

Hypoxanthine–guanine phosphoribosyltransferase (HPRT) deficiency results in a continuous spectrum of clinical phenotypes though all include overproduction of uric acid with hyperuricaemia, urate nephrolithiasis and gout. HPRT1 mutations that result in very low or no HPRT enzyme activities are genera...

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Detalhes bibliográficos
Publicado no:JIMD Rep
Main Authors: Bayat, Allan, Christensen, Mette, Wibrand, Flemming, Duno, Morten, Lund, Allan
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Berlin Heidelberg 2014
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4361920/
https://ncbi.nlm.nih.gov/pubmed/25366392
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2014_368
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