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Synonymous Codon Usage Affects the Expression of Wild Type and F508del CFTR

The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion channel composed of 1480 amino acids. The major mutation responsible for cystic fibrosis results in loss of amino acid residue, F508, (F508del). Loss of F508 in CFTR alters the folding pathway resulting in endoplasmic reticul...

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Kaydedildi:
Detaylı Bibliyografya
Yayımlandı:J Mol Biol
Asıl Yazarlar: Shah, Kalpit, Cheng, Yi, Hahn, Brian, Bridges, Robert, Bradbury, Neil, Mueller, David M.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 2015
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC4355305/
https://ncbi.nlm.nih.gov/pubmed/25676312
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jmb.2015.02.003
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