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Synonymous Codon Usage Affects the Expression of Wild Type and F508del CFTR

The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion channel composed of 1480 amino acids. The major mutation responsible for cystic fibrosis results in loss of amino acid residue, F508, (F508del). Loss of F508 in CFTR alters the folding pathway resulting in endoplasmic reticul...

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Detalhes bibliográficos
Publicado no:J Mol Biol
Main Authors: Shah, Kalpit, Cheng, Yi, Hahn, Brian, Bridges, Robert, Bradbury, Neil, Mueller, David M.
Formato: Artigo
Idioma:Inglês
Publicado em: 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4355305/
https://ncbi.nlm.nih.gov/pubmed/25676312
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jmb.2015.02.003
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