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Detection of ubiquitinated huntingtin species in intracellular aggregates

Protein conformation diseases, including polyglutamine (polyQ) diseases, result from the accumulation and aggregation of misfolded proteins. Huntington’s disease (HD) is one of nine diseases caused by an expanded polyQ repeat within the affected protein and is hallmarked by intracellular inclusion b...

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Vydáno v:Front Mol Neurosci
Hlavní autoři: Juenemann, Katrin, Wiemhoefer, Anne, Reits, Eric A.
Médium: Artigo
Jazyk:Inglês
Vydáno: Frontiers Media S.A. 2015
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4309157/
https://ncbi.nlm.nih.gov/pubmed/25674046
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2015.00001
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