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Detection of ubiquitinated huntingtin species in intracellular aggregates

Protein conformation diseases, including polyglutamine (polyQ) diseases, result from the accumulation and aggregation of misfolded proteins. Huntington’s disease (HD) is one of nine diseases caused by an expanded polyQ repeat within the affected protein and is hallmarked by intracellular inclusion b...

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Detaylı Bibliyografya
Yayımlandı:Front Mol Neurosci
Asıl Yazarlar: Juenemann, Katrin, Wiemhoefer, Anne, Reits, Eric A.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Frontiers Media S.A. 2015
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC4309157/
https://ncbi.nlm.nih.gov/pubmed/25674046
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2015.00001
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