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ER stress and unfolded protein response in amyotrophic lateral sclerosis—a controversial role of protein disulphide isomerase

Accumulation of proteins in aberrant conformation occurs in many neurodegenerative diseases. Furthermore, dysfunctions in protein handling in endoplasmic reticulum (ER) and the following ER stress have been implicated in a vast number of diseases, such as amyotrophic lateral sclerosis (ALS). During...

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Pubblicato in:Front Cell Neurosci
Autori principali: Jaronen, Merja, Goldsteins, Gundars, Koistinaho, Jari
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4251436/
https://ncbi.nlm.nih.gov/pubmed/25520620
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fncel.2014.00402
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