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Deoxyadenosine triphosphate as a potentially toxic metabolite in adenosine deaminase deficiency.
The inherited deficiency of adenosine deaminase (adenosine aminohydrolase; EC 3.5.4.4) activity in humans is associated with an immunodeficiency. Some of the immunodeficient and enzyme-deficient patients respond immunologically to periodic infusions of irradiated erythrocytes containing adenosine de...
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| Publicado en: | Proc Natl Acad Sci U S A |
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| Autores principales: | , , , , , , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
National Academy of Sciences
1978
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC411272/ https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/272665/ https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.75.1.472 |
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