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Deoxyadenosine triphosphate as a potentially toxic metabolite in adenosine deaminase deficiency.

The inherited deficiency of adenosine deaminase (adenosine aminohydrolase; EC 3.5.4.4) activity in humans is associated with an immunodeficiency. Some of the immunodeficient and enzyme-deficient patients respond immunologically to periodic infusions of irradiated erythrocytes containing adenosine de...

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Autors principals: Cohen, A, Hirschhorn, R, Horowitz, S D, Rubinstein, A, Polmar, S H, Hong, R, Martin, D W
Format: Artigo
Idioma:Inglês
Publicat: 1978
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC411272/
https://ncbi.nlm.nih.gov/pubmed/272665
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