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Lung Phenotype of Juvenile and Adult Cystic Fibrosis Transmembrane Conductance Regulator–Knockout Ferrets

Chronic bacterial lung infections in cystic fibrosis (CF) are caused by defects in the CF transmembrane conductance regulator chloride channel. Previously, we described that newborn CF transmembrane conductance regulator–knockout ferrets rapidly develop lung infections within the first week of life....

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Autori principali: Sun, Xingshen, Olivier, Alicia K., Liang, Bo, Yi, Yaling, Sui, Hongshu, Evans, Turan I. A., Zhang, Yulong, Zhou, Weihong, Tyler, Scott R., Fisher, John T., Keiser, Nicholas W., Liu, Xiaoming, Yan, Ziying, Song, Yi, Goeken, J. Adam, Kinyon, Joann M., Fligg, Danielle, Wang, Xiaoyan, Xie, Weiliang, Lynch, Thomas J., Kaminsky, Paul M., Stewart, Zoe A., Pope, R. Marshall, Frana, Timothy, Meyerholz, David K., Parekh, Kalpaj, Engelhardt, John F.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Thoracic Society 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4068938/
https://ncbi.nlm.nih.gov/pubmed/24074402
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1165/rcmb.2013-0261OC
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