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Bioelectric Characterization of Epithelia from Neonatal CFTR Knockout Ferrets

Cystic fibrosis (CF) is a life-shortening, recessive, multiorgan genetic disorder caused by the loss of CF transmembrane conductance regulator (CFTR) chloride channel function found in many types of epithelia. Animal models that recapitulate the human disease phenotype are critical to understanding...

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Dettagli Bibliografici
Autori principali: Fisher, John T., Tyler, Scott R., Zhang, Yulong, Lee, Ben J., Liu, Xiaoming, Sun, Xingshen, Sui, Hongshu, Liang, Bo, Luo, Meihui, Xie, Weiliang, Yi, Yaling, Zhou, Weihong, Song, Yi, Keiser, Nicholas, Wang, Kai, de Jonge, Hugo R., Engelhardt, John F.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Thoracic Society 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3931095/
https://ncbi.nlm.nih.gov/pubmed/23782101
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1165/rcmb.2012-0433OC
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