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The cockayne syndrome B protein is essential for neuronal differentiation and neuritogenesis

Cockayne syndrome (CS) is a progressive developmental and neurodegenerative disorder resulting in premature death at childhood and cells derived from CS patients display DNA repair and transcriptional defects. CS is caused by mutations in csa and csb genes, and patients with csb mutation are more pr...

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Detalhes bibliográficos
Main Authors: Ciaffardini, F, Nicolai, S, Caputo, M, Canu, G, Paccosi, E, Costantino, M, Frontini, M, Balajee, A S, Proietti-De-Santis, L
Formato: Artigo
Idioma:Inglês
Publicado em: Nature Publishing Group 2014
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4047889/
https://ncbi.nlm.nih.gov/pubmed/24874740
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/cddis.2014.228
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