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Wiskott–Aldrich Syndrome protein deficiency perturbs the homeostasis of B-cell compartment in humans()

Wiskott–Aldrich Syndrome protein (WASp) regulates the cytoskeleton in hematopoietic cells and mutations in its gene cause the Wiskott–Aldrich Syndrome (WAS), a primary immunodeficiency with microthrombocytopenia, eczema and a higher susceptibility to develop tumors. Autoimmune manifestations, freque...

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Detaylı Bibliyografya
Asıl Yazarlar: Castiello, Maria Carmina, Bosticardo, Marita, Pala, Francesca, Catucci, Marco, Chamberlain, Nicolas, van Zelm, Menno C., Driessen, Gertjan J., Pac, Malgorzata, Bernatowska, Ewa, Scaramuzza, Samantha, Aiuti, Alessandro, Sauer, Aisha V., Traggiai, Elisabetta, Meffre, Eric, Villa, Anna, van der Burg, Mirjam
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Academic Press 2014
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC4012141/
https://ncbi.nlm.nih.gov/pubmed/24369837
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jaut.2013.10.006
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