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Progesterone Antagonist Therapy in a Pelizaeus-Merzbacher Mouse Model

Pelizaeus-Merzbacher disease (PMD) is a severe hypomyelinating disease, characterized by ataxia, intellectual disability, epilepsy, and premature death. In the majority of cases, PMD is caused by duplication of PLP1 that is expressed in myelinating oligodendrocytes. Despite detailed knowledge of PLP...

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Detaylı Bibliyografya
Asıl Yazarlar: Prukop, Thomas, Epplen, Dirk B., Nientiedt, Tobias, Wichert, Sven P., Fledrich, Robert, Stassart, Ruth M., Rossner, Moritz J., Edgar, Julia M., Werner, Hauke B., Nave, Klaus-Armin, Sereda, Michael W.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Elsevier 2014
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC3980417/
https://ncbi.nlm.nih.gov/pubmed/24680886
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ajhg.2014.03.001
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