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The de-ubiquitinating enzyme ataxin-3 does not modulate disease progression in a knock-in mouse model of Huntington disease

Ataxin-3 is a deubiquitinating enzyme (DUB) that participates in ubiquitin-dependent protein quality control pathways and, based on studies in model systems, may be neuroprotective against toxic polyglutamine proteins such as the Huntington's disease (HD) protein, huntingtin (htt). HD is one of...

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Detaylı Bibliyografya
Asıl Yazarlar: Zeng, Li, Tallaksen-Greene, Sara J., Wang, Bo, Albin, Roger L., Paulson, Henry L.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 2013
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC3966139/
https://ncbi.nlm.nih.gov/pubmed/24683430
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/JHD-130058
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