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Laminin-111 improves muscle repair in a mouse model of merosin-deficient congenital muscular dystrophy

Merosin-deficient congenital muscular dystrophy type 1A (MDC1A) is a severe and fatal muscle-wasting disease with no cure. MDC1A patients and the dy(W−/−) mouse model exhibit severe muscle weakness, demyelinating neuropathy, failed muscle regeneration and premature death. We have recently shown that...

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Autors principals: Van Ry, Pam M., Minogue, Priscilla, Hodges, Bradley L., Burkin, Dean J.
Format: Artigo
Idioma:Inglês
Publicat: Oxford University Press 2014
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3869356/
https://ncbi.nlm.nih.gov/pubmed/24009313
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddt428
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