Caricamento...

Laminin-111 protein therapy prevents muscle disease in the mdx mouse model for Duchenne muscular dystrophy

Duchenne muscular dystrophy (DMD) is a devastating neuromuscular disease caused by mutations in the gene encoding dystrophin. Loss of dystrophin results in reduced sarcolemmal integrity and increased susceptibility to muscle damage. The α(7)β(1)-integrin is a laminin-binding protein up-regulated in...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Autori principali: Rooney, Jachinta E., Gurpur, Praveen B., Burkin, Dean J.
Natura: Artigo
Lingua:Inglês
Pubblicazione: National Academy of Sciences 2009
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2683113/
https://ncbi.nlm.nih.gov/pubmed/19416897
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0811599106
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !