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Intestinal HIF2α promotes tissue-iron accumulation in disorders of iron overload with anemia

Several distinct congenital disorders can lead to tissue-iron overload with anemia. Repeated blood transfusions are one of the major causes of iron overload in several of these disorders, including β-thalassemia major, which is characterized by a defective β-globin gene. In this state, hyperabsorpti...

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Autors principals: Anderson, Erik R., Taylor, Matthew, Xue, Xiang, Ramakrishnan, Sadeesh K., Martin, Angelical, Xie, Liwei, Bredell, Bryce X., Gardenghi, Sara, Rivella, Stefano, Shah, Yatrik M.
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 2013
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3864280/
https://ncbi.nlm.nih.gov/pubmed/24282296
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1314197110
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