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Depletion of extracellular signal-regulated kinase 1 in mice with cardiomyopathy caused by lamin A/C gene mutation partially prevents pathology before isoenzyme activation

Mutations in the lamin A/C gene (LMNA) encoding A-type nuclear lamins cause dilated cardiomyopathy with variable muscular dystrophy. These mutations enhance mitogen-activated protein kinase signaling in the heart and pharmacological inhibition of extracellular signal-regulated kinase (ERK) 1 and 2 i...

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Autors principals: Wu, Wei, Iwata, Shinichi, Homma, Shunichi, Worman, Howard J., Muchir, Antoine
Format: Artigo
Idioma:Inglês
Publicat: Oxford University Press 2014
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3857940/
https://ncbi.nlm.nih.gov/pubmed/23933734
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddt387
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