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Structural Features of the Regulatory ACT Domain of Phenylalanine Hydroxylase

Phenylalanine hydroxylase (PAH) catalyzes the conversion of L-Phe to L-Tyr. Defects in PAH activity, caused by mutations in the human gene, result in the autosomal recessively inherited disease hyperphenylalaninemia. PAH activity is regulated by multiple factors, including phosphorylation and ligand...

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Autori principali: Carluccio, Carla, Fraternali, Franca, Salvatore, Francesco, Fornili, Arianna, Zagari, Adriana
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3828330/
https://ncbi.nlm.nih.gov/pubmed/24244510
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0079482
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