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Cortical metabolism in pyruvate dehydrogenase deficiency revealed by ex vivo multiplet (13)C-NMR of the adult mouse brain

The pyruvate dehydrogenase complex (PDC), required for complete glucose oxidation, is essential for brain development. Although PDC deficiency is associated with a severe clinical syndrome, little is known about its effects on either substrate oxidation or synthesis of key metabolites such as glutam...

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Detalhes bibliográficos
Main Authors: Marin-Valencia, Isaac, Good, Levi B., Ma, Qian, Malloy, Craig R., Patel, Mulchand S., Pascual, Juan M.
Formato: Artigo
Idioma:Inglês
Publicado em: 2012
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3816779/
https://ncbi.nlm.nih.gov/pubmed/22884585
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.neuint.2012.07.020
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